Download fulltext pdf chondromyxoid fibroma involving the sphenoid sinus. Chondromyxoid fibroma of frontal bone is a rare lesion. In rare cases, however, cmf presents in unusual locations, such as the facial bones and sinonasal tract. Download free adobe acrobat reader dc software for your windows, mac os and android devices to view, print, and comment on pdf documents. A rare and benign chondrogenic lesion characterized by variable amounts of chondroid, fibromatoid and myxoid elements. Chondromyxoid fibroma cmf is a rare benign neoplasm of cartilaginous origin and represents less than 1% of all primary tumors of bone.
Chondromyxoid fibroma is a rare benign bone tumor accounting for approximately 1% of all benign bone tumors. At a 6month followup the patient remained free of recurrence. An eccentric, radiolucent destructive lesion with a thin rim of reactive bone was noted. Chondromyxoid fibroma cmf is one of the rarest of bone tumors, accounting for less than 1% of all bone tumors.
Chondroblastoma and chondromyxoid fibroma 226 journal of the american academy of orthopaedic surgeons. Fibrous cortical defect, nonossifying fibroma portnotes. The decisive role played by the radiologist in identifying the benign nature of the lesion is emphasized. We report the second case of desmoplastic fibroma of bone with extensive chondroid metaplasia. Famous quote experience is a good teacher, but she sends in terrific bills. It is a benign noncancerous tumor that most often develops in older children and young adults under 30 years of age. As with all rare lesions, reported epidemiology varies. In a patient of this age, paraosteal chondrosarcoma should be excluded. Pdf chondromyxoid fibroma involving the sphenoid sinus. Juxtacortical chondromyxoid fibroma of tibia sam hajialiloo sami, tina shooshtarizadeh, hajar zekavat and mehrdad bahrabadi bone and joint reconstruction research center, iran university of.
Chondromyxoid fibroma is a type of cartilaginous tumor most cases are characterised by grm1 gene fusion or promoter swapping. Rare in the upper limb and in the trunk besides pelvis. Mr images of 19 histopathologically confirmed chondromyxoid fibromas were retrospectively analyzed for signal. The diagnosis of cmf depends upon its characteristic histological appearance like a lobular pattern with stellateshaped cells in a myxoid or. Feldman f, hecht hl, johnston ad 1970 chondromyxoid fibroma of bone. We report the fourth case of chondromyxoid fibroma of the sternum described in the literature. Accounting for less than 1% of all bone tumors and 2% of benign bone tumors, cmf presents as a locally destructive lesion usually in the 2nd to 3rd decade, although cases have presented. Chondromyxoid fibroma cmf is a benign cartilaginous neoplasm first distinguished from other cartilaginous tumors by jaffe and lichenstein in 1948.
Treatment for cmf requires surgery to remove the tumor. Upon history taking, we found that the mass had formed 7 to 8 years before and had since grown slowly. Chondromyxoid fibroma of the distal fibula in a pediatric. On mri, chondromyxoid fibroma shows a multilobulated pattern, with low signal intensity on t1weighted images and high signal intensity on t2weighted images. Well circumscribed, hypocellular lobules of poorly formed hyaline cartilage composed of chondroblasts with abundant pink cytoplasm and myxoid tissue with fibrous septae containing spindle cells and osteoclasts. Chondromyxoid fibroma of the frontal bone tatsuo morimura, 12 atsuhisa nakano, 1 tsuyoshi matsumoto, 1 and eiichi tani1 summary. Typically located in the long bone metaphysis, it can invade the epiphysis, especially in adults. Most cases of cmf occur in the metaphysis of tubular bones of the lower extremity. Desmoplastic fibroma of bone with extensive cartilaginous. Acta otorrinolaringologica english edition volume 60, issue 1, 2009, pages 7072. The aim of this study was to assess and present the radiological morphology of the nonossifying fibroma nof, to describe the life span according to the ritschlstages in an effort to determine critical stages with regard to pathological fractures and discuss the need for a followup. Preferred sites proximal tibia 30 % of cases, small bones of the foot, and pelvis.
Full text full text is available as a scanned copy of the original print version. Chondromyxoid fibroma cmf is an exceedingly rare benign tumor of cartilaginous origin accounting for less than 1% of all primary bone tumors and less than 2% of benign bone tumors. Various treatment options are available for this tumour and recurrences have been reported following surgery. A rare case of chondromyxoid fibroma of the scapula. Chondromyxoid fibroma clubfoot congenital scoliosis developmental dysplasia of the hip ddh discoid meniscus down syndrome early onset scoliosis eos flexible flat feet hemangioma intoeing juvenile arthritis kyphosis leg length discrepancy marfan syndrome muscular dystrophy musculoskeletal infections. They do not become cancerous and they do not spread metastasize. Links to pubmed are also available for selected references. Eight new cases are added, 4 of which exhibited unusual size andor focal microscopic calcification, pathologic fracture, diaphyseal location. Chondromyxoid fibroma of the finger pubmed central pmc. Chondromyxoid fibroma is a benign tumor composed of spindle or stellate cells forming lobules and with abundant myxoid andor chondroid intercellular material. One very infrequent type is sclerotic fibromalike df sf. Chondromyxoid fibroma presents as a bigger, lucent, loculated lesion with a sharp sclerotic margin in the metaphysis of long bones. A read is counted each time someone views a publication summary such as the title, abstract, and list of authors, clicks on a figure, or views or downloads the fulltext. Chondromyxoid fibroma cmf is one of the rarest benign tumors of cartilaginous origin.
Chondromyxoid fibroma of the scapula occurring in a 23 year old. A 35yearold man visited us with a chief complaint of painful swelling of the finger. Get a printable copy pdf file of the complete article 647k, or click on a page image below to browse page by page. Typically patients present with progressive pain, often long. With contrast injection, the central portion of the lesion may show no enhancement due to the myxoid component.
The craniofacial region is affected in only 2% of cases. Chondromyxoid fibroma cmf, believed to be of cartilaginous derivation, is a benign chondroid and myxoid matrixproducing tumor that is occasionally seen in association with fibrous areas. Resources for fibrous cortical defect, nonossifying fibroma and related topics on orthopaedicsone. Adobe acrobat reader dcdownload kostenloser pdfviewer fur. Pdfreader, pdfviewer kostenlos adobe acrobat reader dc. Chondromyxoid fibroma cmf is a rare benign cartilaginous tumor that usually arises from the metaphysis of long bones. Chondromyxoid fibroma cmf is a benign cartilaginous tumour which involves mainly the long bones and proximal tibia being common.
Juvenile aponeurotic fibroma was first described as a tumor occurring in the palms and soles of young children. Chondromyxoid fibroma of the distal fibula in a pediatric patient. Nonossifying fibromas nofs are the most common benign bone tumor in children. Desmoplastic fibroma of bone is a rare tumor demonstrating the same histologic and biologic features of its soft tissue counterpart, aggressive fibromatosis. To describe the mr findings of chondromyxoid fibroma. It is more commonly seen during the second and third decades of life.
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